Nutrition for Glycogen Storage Disease - Ingredients to Avoid and Ingredients Allowed

These instructions are for caregivers of Children's Hospital of Philadelphia patients who have glycogen storage disease (GSD).

Important information:

Learn more about glycogen storage disease.

Patient instructions ingredients to avoid:

• Fructose

• Galactose

• Lactose

• Sucrose

• Saccharose

• Honey

• High-fructose corn syrup

• Corn syrup (contains fructose)

• Beet sugar

• Brown sugar

• Cane sugar

• Invert sugar

• Agave nectar/syrup

• Maple sugar

• Powdered sugar

• Raw sugar

• Caramel

• Carob

• Maple syrup

• Molasses

• Sorghum

• Turbinado

• Casein

• Whey

• Sorbitol

Patient instructions ingredients allowed:

• Glucose

• Dextrose

• Maltose

• Maltodextrin

• Dextrin

• Barley syrup

• Brown rice syrup

• Tapioca syrup

• Pure corn syrup

• Corn syrup solids

• Karo dark corn syrup (98% glucose)

• Karo light corn syrup (97% glucose)

• Karo pancake syrup (94% glucose)

• Sweet ‘N Low (saccharin)

• Equal (aspartame)

• Splenda (sucralose)

• Stevia

• Truvia

• Xylitol

• Mannitol

• Erythritol

• Hydrogenated starch hydrolysates

Call your CHOP team with any questions or concerns.

Division of Endocrinology and Diabetes

Reviewed on February 14, 2023, by Heather McKnight, CRNP; Nicole Stewart, RN